Multiple Gastro Intestinal Lymphangiomatosis - Case Report
Keywords:
LymphangiomatosisAbstract
Lymphangiomatosis is a result of congenital errors of lymphatic development which takes place before 20 weeks of gestation. By definition, Lymphangiomatosis is a benign soft tissue tumour of lymphatic channels. We present one such case of lymphangiomatosis which involved multiple gastrointestinal organs. Lymphangiomatosis is a rare entity which is rarely seen and belongs to a spectrum of developmental disorders. Recognition of the disease requires a high index of suspicion and an extensive workup. Because of its serious morbidity, lymphangiomatosis must always be considered in the list of our differential diagnosis.
References
Ramani P, Shah A. Lymphangiomatosis. Histologic and immunohistochemical analysis of four cases. Am J Surg Pathol 1993;17:329-35. Back to cited text no.
Gomez CS, Calonje E, ferrar DW, Browse NL, Fletcher CD. Lymphangiomatosis of the limbs. Clinicopathologic analysis of a series with a good prognosis. Am J Surg Pathol 1995;19:125-33.
Rao VK, Weiss SW. Angiomatosis of soft tissue: An analysis of histologic features and clinical outcome in 51 cases. Am J Surg Pathol 1992;16:764-71.
Venkatramani R, Ma NS, Pitukcheewanont P, Malogolowkin MH, Mascarenhas L. Gorham’s disease and diffuse lymphangiomatosis in children and adolescents. Pediatr Blood Cancer. 2011 Apr;56(4):667-70
CS Wong, TYC Chu. Clinical and radiological features of generalised lymphangiomatosis. Hong Kong Med J 2008;14:402-4
O’Sullivan DA, Torres VE, de Groen PC, Batts KP, King BF, Vockley J. "Hepatic lymphangiomatosis mimicking polycystic liver disease. Mayo Clin Proc. 1998 Dec;73(12):1188-92.
Yeager ND, Hammond S, Mahan J, Davis JT, Adler B. Unique diagnostic features and successful management of a patient with disseminated lymphangiomatosis and chylothorax. J Pediatr Hematol Oncol. 2008 Jan;30(1):66-9.
Zisis C, Spiliotopoulos K, Patronis M, Filippakis G, Stratakos G, Tzelepis G, et al. Diffuse lymphangiomatosis: Are there any clinical or therapeutic
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