Rare Presentation of Primary Uterine Teratoma with Congenital Unilateral Renal Agenesis: A Case Report


  • Sanini Sarah Department of Obstetrics and Gynaecology, Faculty of Health Sciences, Busitema University, Uganda.
  • Nteziyaremye Julius Department of Obstetrics and Gynaecology, Mbale Regional Referral Hospital, Uganda. https://orcid.org/0000-0002-6286-2867


unilateral renal agenesis, uterine teratoma, case report


Introduction: In gynaecology, uterine teratomas are quite uncommon. The indications and symptoms being vague, its presentation might be difficult to identify. It very seldom coexists with Congenital Unilateral Renal Agenesis (CURA). We describe a rare instance of extragonadal uterine teratoma with congenital unilateral renal agenesis in a 20-year-old nulliparous female who arrived at a tertiary care facility in eastern Uganda with vague signs and symptoms.
Case Presentation: A district hospital referred a 20-year-old nulliparous woman who had a four-year history of urinary blockage and symptoms of overflow incontinence and hesitation. Later, she had menorrhagia, dysmenorrhoea, and irregular uterine bleeding. She was found to be terribly pale and unwell upon inspection, and her blood pressure was measured at 150/90 mmHg. She was discovered to have an abnormal uterine haemorrhage, severe anaemia, congenital unilateral renal agenesis, chronic renal failure with obstructive uropathy, and uterine teratoma. She was managed on repeated blood transfusions and empirical management with antihypertensive drugs, salt and fluid restriction, and antibiotics for chronic renal disease with obstructive uropathy.
She was managed on repeated blood transfusions and empirical management with antihypertensive drugs, salt and fluid restriction, and antibiotics for chronic renal disease with obstructive uropathy.
Conclusion: The association of congenital unilateral renal agenesis with uterine teratomas affecting the corpus, cervix, and fundus is uncommon, despite the few examples of these lesions that have been reported. Additionally, it has been noted that the Mayer-Rokitansky-Kuster-Hauser (MRKH) syndrome frequently coexists with instances of renal agenesis. Hence, we encourage gynaecologists to be aware of uterine teratoma as a potential cause of irregular uterine bleeding in women of reproductive age. Additionally, if a patient presents with urinary bladder blockage or other uropathy-related symptoms, one should consider the possibility of congenital urinary diseases. Consideration should be given to collaborative management with a urologist.

How to cite this article:
Sarah S, Julius N. Rare Presentation of Primary Uterine Teratoma with Congenital Unilateral Renal Agenesis: A Case Report. Int J Adv Res Gynaecol Obstet. 2023;1(2):31-39.


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